ASN's Mission

To create a world without kidney diseases, the ASN Alliance for Kidney Health elevates care by educating and informing, driving breakthroughs and innovation, and advocating for policies that create transformative changes in kidney medicine throughout the world.

learn more

Contact ASN

1401 H St, NW, Ste 900, Washington, DC 20005

email@asn-online.org

202-640-4660

The Latest on X

Kidney Week

Abstract: FR-PO0383

Uncommon Presentations of Primary Aldosteronism: Edema and Hormonal Cosecretion

Session Information

Category: Hypertension and CVD

  • 1602 Hypertension and CVD: Clinical

Authors

  • Alam, Sreyoshi Fatima, Mayo Clinic Minnesota, Rochester, Minnesota, United States
  • Young, William F., Mayo Clinic Minnesota, Rochester, Minnesota, United States
  • Garovic, Vesna D., Mayo Clinic Minnesota, Rochester, Minnesota, United States
Introduction

Primary aldosteronism (PA), classically defined by hypertension and hypokalemia, can present atypically with normotension, edema, or hormonal co-secretion. We present two such cases: one in a normotensive, lean woman with chronic edema, and the other in a hypertensive woman with cortisol co-secretion from a right adrenal aldosterone-producing adenoma (APA). These cases expand PA’s clinical spectrum and highlight the importance of individualized evaluation.

Case Description

Case 1: Normotensive PA with Chronic Edema
A 49-year-old woman (BMI 18.3) developed mild hypertension, treated with thiazide diuretics, resulting in hypokalemia. Her BP normalized, thiazide was stopped, but peripheral edema persisted. Labs showed PAC 29.6 ng/dL and PRA 0.5 ng/mL/hr. Imaging was initially read as negative, but re-review revealed left adrenal micronodularity. She chose medical therapy with eplerenone, titrated to achieve PRA >1 ng/mL/hr and normokalemia.
Case 2: Cortisol Co-Secreting Right Adrenal APA in Hypertensive Woman
A 41-year-old woman developed hypokalemia in the third trimester of pregnancy, later diagnosed with postpartum hypertension and persistent edema. Ongoing BP and potassium fluctuations prompted endocrine workup. Initial labs: PAC 21.8 ng/dL, PRA 0.5; repeat: PAC 20.6, PRA 0.9; 24-hour urine aldosterone: 25.8 mcg on high sodium diet (442 mEq). DHEA-S remained consistently low (15–16 mcg/dL), suggesting chronic corticotropin suppression and cortisol co-secretion. A 1-mg dexamethasone suppression test (DST) showed abnormal cortisol (2.7 mcg/dL); 8-mg DST confirmed subclinical hypercortisolism (17.9 mcg/dL). Adrenal vein sampling (AVS) showed marked cortisol and aldosterone lateralization to the right adrenal (cortisol: 1190 vs. 174 mcg/dL; aldosterone: 15,000 vs. 1872 ng/dL), consistent with a right adrenal APA with cortisol co-secretion. CT showed a 1.1 cm lipid-rich right adrenal nodule. She underwent laparoscopic right adrenalectomy.

Discussion

These cases illustrate atypical PA presentations. The first shows that PA can exist without hypertension, presenting as edema from aldosterone-driven volume expansion. The second underscores evaluating cortisol co-secretion in PA with adrenal adenomas, as it affects AVS interpretation and management. Both highlight the need for diagnostic approaches beyond the classical PA phenotype.

Digital Object Identifier (DOI)