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Kidney Week

Abstract: SA-PO0186

Autologous Stem-Cell Transplant for Management of Monoclonal Gammopathy of Renal Significance

Session Information

Category: Onconephrology

  • 1700 Onconephrology

Authors

  • Maharaj, Sime, Weill Cornell Medicine, New York, New York, United States
  • Seshan, Surya V., Weill Cornell Medicine, New York, New York, United States
  • Glezerman, Ilya, Memorial Sloan Kettering Cancer Center, New York, New York, United States
Introduction

Monoclonal gammopathy of renal significance (MGRS) is a clonal proliferative disease characterized by nephrotoxic proteins leading to various kidney pathologies. MGRS lacks non-renal manifestations of plasma cell dyscrasias. Treatment aims to preserve kidney function and eradicate the malignant clone. We present a case of MGRS associated with proximal tubular light chain deposition treated with autologous stem cell transplant (ASCT).

Case Description

A 64 year old male presented to renal clinic with elevated serum creatinine (SCr) 1.5 mg/dL (0.6-1.3) noted 6 months ago, from a baseline of 1.0 mg/dL. His only complaint was nocturia. Two years prior to presentation, he was diagnosed with a solitary plasmacytoma of the C6 vertebra. Bone marrow biopsy showed minimal involvement by plasma cell neoplasm, <5% involvement by CD138 immunohistochemistry with kappa light chain restriction. He underwent resection followed by radiation. Physical exam was unremarkable. Remaining labs were significant for kappa free light chains (kFLC) 38.9 mg/dL and kappa to lambda ratio (k/L) of 35.93. Urinalysis was bland, without proteinuria. Patient was observed until 10 months after clinic presentation, when urine protein to creatinine ratio rose to 0.6, with kFLC of 84.07mg/dL and k/L of 76.43. sCr was 1.6 mg/dL. Kidney biopsy revealed diffuse proximal tubulopathy, with monoclonal kappa light chain restriction, crystalline and non crystalline deposits (light chain proximal tubulopathy) and occasional glomerular epithelial involvement (Fig 1). His renal function and proteinuria worsened, therefore he underwent six cycles of daratumumab, cyclophosphamide, bortezomib and dexamethasone followed by ASCT. Six months later, kFLC improved to 0.59 mg/dL and proteinuria resolved. sCr returned to a new baseline of 1.2 mg/dL.

Discussion

Our case illustrates that chemotherapy and ASCT can successfully treat MGRS, leading to reversal of kidney dysfunction.

Digital Object Identifier (DOI)